Celiac disease is characterized by intestinal inflammation and mucosal atrophy that improves on a gluten-free diet. Delayed diagnosis can result in diet-refractory disease known as refractory sprue, which is linked to other disorders (intestinal lymphoma, ulcerative jejunoileitis, mesenteric lymph-node cavitation, collagenous sprue, malignancy) and carries a poor prognosis. Here we report the case of a young woman diagnosed with Marsh stage 3C celiac disease with intestinal occlusion due to intra-abdominal cystic lymphangioma mimicking mesenteric lymph-node cavitation, and hyposplenism. Despite a number of prognostically negative features, the disease has been managed successfully for the past 2 years with a gluten-free diet. The pathogenesis, prognosis and therapeutic implications are discussed.

Miele, L., Pierconti, F., Forgione, A., Vero, V., Molinari, F., Cammarota, G., Masselli, G., Capristo, E., Martini, M., Larocca, L. M., Civello, I. M., Gasbarrini, G. B., Grieco, A., Cystic lymphangioma of the mesentery and hyposplenism in celiac disease., <<EUROPEAN JOURNAL OF GASTROENTEROLOGY & HEPATOLOGY>>, 2007; (Novembre): 1026-1030 [http://hdl.handle.net/10807/16427]

Cystic lymphangioma of the mesentery and hyposplenism in celiac disease.

Miele;Luca; Pierconti;Francesco; Forgione;Alessandra; Vero;Vittoria; Molinari;Francesco; Cammarota;Giovanni; Masselli;Gabriele; Capristo;Esmeralda; Martini;Maurizio; Larocca;Luigi Maria; Civello;Ignazio Massimo; Gasbarrini;Giovanni Battista; Grieco
2007

Abstract

Celiac disease is characterized by intestinal inflammation and mucosal atrophy that improves on a gluten-free diet. Delayed diagnosis can result in diet-refractory disease known as refractory sprue, which is linked to other disorders (intestinal lymphoma, ulcerative jejunoileitis, mesenteric lymph-node cavitation, collagenous sprue, malignancy) and carries a poor prognosis. Here we report the case of a young woman diagnosed with Marsh stage 3C celiac disease with intestinal occlusion due to intra-abdominal cystic lymphangioma mimicking mesenteric lymph-node cavitation, and hyposplenism. Despite a number of prognostically negative features, the disease has been managed successfully for the past 2 years with a gluten-free diet. The pathogenesis, prognosis and therapeutic implications are discussed.
Inglese
Miele, L., Pierconti, F., Forgione, A., Vero, V., Molinari, F., Cammarota, G., Masselli, G., Capristo, E., Martini, M., Larocca, L. M., Civello, I. M., Gasbarrini, G. B., Grieco, A., Cystic lymphangioma of the mesentery and hyposplenism in celiac disease., <<EUROPEAN JOURNAL OF GASTROENTEROLOGY & HEPATOLOGY>>, 2007; (Novembre): 1026-1030 [http://hdl.handle.net/10807/16427]
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/10807/16427
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