Familial Mediterranean fever is an autosomal recessive disorder characterized by transient attacks of fever and polyserositis with substantial risk of developing amyloidotic nephropathy over time. We report an Italian child with familial Mediterranean fever presenting with hematuria during attacks in whom kidney biopsy documented the presence of mesangial IgA deposits and the absence of amyloidosis. Kidney biopsy should be performed in patients showing microscopic or gross hematuria during attacks of familial Mediterranean fever in order to gain additional epidemiological data about specific features of renal involvement and to allow adequate treatment.

Rigante, D., Federico, G., Ferrara, P., Maggiano, N. G., Avallone, L., Pugliese, A. L., Stabile, A., IgA nephropathy in an Italian child with familial Mediterranean fever, <<PEDIATRIC NEPHROLOGY>>, 2005; (20): 1642-1644. [doi:10.1007/s00467-005-2023-5] [http://hdl.handle.net/10807/3663]

IgA nephropathy in an Italian child with familial Mediterranean fever

Rigante, Donato;Federico, Gilda;Ferrara, Pietro;Maggiano, Nicola Giuseppe;Avallone, Laura;Pugliese, Anna Lisa;Stabile, Achille
2005

Abstract

Familial Mediterranean fever is an autosomal recessive disorder characterized by transient attacks of fever and polyserositis with substantial risk of developing amyloidotic nephropathy over time. We report an Italian child with familial Mediterranean fever presenting with hematuria during attacks in whom kidney biopsy documented the presence of mesangial IgA deposits and the absence of amyloidosis. Kidney biopsy should be performed in patients showing microscopic or gross hematuria during attacks of familial Mediterranean fever in order to gain additional epidemiological data about specific features of renal involvement and to allow adequate treatment.
Inglese
Rigante, D., Federico, G., Ferrara, P., Maggiano, N. G., Avallone, L., Pugliese, A. L., Stabile, A., IgA nephropathy in an Italian child with familial Mediterranean fever, <<PEDIATRIC NEPHROLOGY>>, 2005; (20): 1642-1644. [doi:10.1007/s00467-005-2023-5] [http://hdl.handle.net/10807/3663]
File in questo prodotto:
Non ci sono file associati a questo prodotto.

I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.

Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/10807/3663
Citazioni
  • ???jsp.display-item.citation.pmc??? ND
  • Scopus 8
  • ???jsp.display-item.citation.isi??? 9
social impact