Diencephalic syndrome (DS) is a relative rare disease characterized by a complex of signs and symptoms secondary to hypothalamic dysfunction. In most cases, this disease is due to low grade gliomas of the anterior hypothalamus or optic nerve. These tumours associated with DS seem to have a more aggressive behaviour than others astrocytomas located in the anterior hypothalamic region. This syndrome should be considered in the differential diagnosis of children with growth failure. It is a condition commonly observed by primary care physicians and it is extremely important to recognize it because of the severity of the conditions which may be associated with it.
Scalzone, M., Coccia, P., Ruggiero, A., Lazzareschi, I., Mastrangelo, S., Riccardi, R., Diencephalic syndrome and brain tumours: A rare cause of growth failure, <<EUROPEAN JOURNAL OF ONCOLOGY>>, 2009; 14 (1): 53-56 [https://hdl.handle.net/10807/297636]
Diencephalic syndrome and brain tumours: A rare cause of growth failure
Ruggiero, Antonio;Lazzareschi, Ilaria;Mastrangelo, Stefano;Riccardi, Riccardo
2009
Abstract
Diencephalic syndrome (DS) is a relative rare disease characterized by a complex of signs and symptoms secondary to hypothalamic dysfunction. In most cases, this disease is due to low grade gliomas of the anterior hypothalamus or optic nerve. These tumours associated with DS seem to have a more aggressive behaviour than others astrocytomas located in the anterior hypothalamic region. This syndrome should be considered in the differential diagnosis of children with growth failure. It is a condition commonly observed by primary care physicians and it is extremely important to recognize it because of the severity of the conditions which may be associated with it.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.