The superficial siderosis (SS) of the central nervous system (CNS) is a rare condition characterized by a wide range of neurological manifestations directly linked to an acquired iron-mediated neurodegeneration. First described more than 100 years ago, only recently SS has been divided into two distinct entities, according to the distribution of iron deposition in the CNS: cortical superficial siderosis (cSS) and infratentorial superficial siderosis (iSS). Here we describe an adult case of iSS, with detailed clinical and radiological features. Moreover, we extensively review the literature of SS, particularly focusing on the pathogenesis, clinical-radiological classification, diagnostic algorithm and treatment options of this rare condition.

Stabile, A., Di Lazzaro, V., Colosimo, C., Piazza, F., Ferrarese, C., Difrancesco, J., Idiopathic infratentorial superficial siderosis of the central nervous system: case report and review of literature., <<NEUROLOGIA I NEUROCHIRURGIA POLSKA>>, 2018; (52(1)): 102-106. [doi:10.1016/j.pjnns.2017.10.006] [http://hdl.handle.net/10807/116675]

Idiopathic infratentorial superficial siderosis of the central nervous system: case report and review of literature.

Stabile, A;Di Lazzaro, V;Colosimo, C;
2017

Abstract

The superficial siderosis (SS) of the central nervous system (CNS) is a rare condition characterized by a wide range of neurological manifestations directly linked to an acquired iron-mediated neurodegeneration. First described more than 100 years ago, only recently SS has been divided into two distinct entities, according to the distribution of iron deposition in the CNS: cortical superficial siderosis (cSS) and infratentorial superficial siderosis (iSS). Here we describe an adult case of iSS, with detailed clinical and radiological features. Moreover, we extensively review the literature of SS, particularly focusing on the pathogenesis, clinical-radiological classification, diagnostic algorithm and treatment options of this rare condition.
Inglese
Stabile, A., Di Lazzaro, V., Colosimo, C., Piazza, F., Ferrarese, C., Difrancesco, J., Idiopathic infratentorial superficial siderosis of the central nervous system: case report and review of literature., <<NEUROLOGIA I NEUROCHIRURGIA POLSKA>>, 2018; (52(1)): 102-106. [doi:10.1016/j.pjnns.2017.10.006] [http://hdl.handle.net/10807/116675]
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Utilizza questo identificativo per citare o creare un link a questo documento: http://hdl.handle.net/10807/116675
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