Brancaccio, Andrea

Brancaccio, Andrea  

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Data di pubblicazione Titolo Autore(i) File
1-gen-2024 Analysis of the GFP-labelled β-dystroglycan interactome in HEK-293 transfected cells reveals novel intracellular networks Sciandra, Francesca; Desiderio, Claudia; Vincenzoni, F.; Viscuso, S.; Bozzi, Manuela; Hubner, W.; Jimenez-Gutierrez, G. E.; Cisneros, B.; Brancaccio, Andrea
1-gen-2024 Missense mutation (C667F) in murine β-dystroglycan causes embryonic lethality, myopathy and blood-brain barrier destabilization Lois Tan, Rui; Sciandra, Francesca; Hübner, Wolfgang; Bozzi, Manuela; Reimann, Jens; Schoch, Susanne; Brancaccio, Andrea; Blaess, Sandra
1-gen-2023 Verbascoside Elicits Its Beneficial Effects by Enhancing Mitochondrial Spare Respiratory Capacity and the Nrf2/HO-1 Mediated Antioxidant System in a Murine Skeletal Muscle Cell Line Sciandra, Francesca; Bottoni, Paola; De Leo, M.; Braca, A.; Brancaccio, Andrea; Bozzi, Manuela
1-gen-2020 Identification and modelling of a GT-A fold in the α-dystroglycan glycosylating enzyme LARGE1 Righino, Benedetta; Bozzi, Manuela; Pirolli, Davide; Sciandra, Francesca; Bigotti, Maria Giulia; Brancaccio, Andrea; De Rosa, Maria Cristina
1-gen-2018 The enzymatic processing of α-dystroglycan by MMP-2 is controlled by two anchoring sites distinct from the active site. Gioia, Magda; Francesco Fasciglione, Giovanni; Sbardella, Diego; Sciandra, Francesca; Casella, Marialuisa; Camerini, Serena; Crescenzi, Marco; Gori, Alessandro; Tarantino, Umberto; Cozza, Paola; Brancaccio, Andrea; Coletta, Massimo; Bozzi, Manuela
1-gen-2017 A dystroglycan mutation (p.Cys667Phe) associated to Muscle-Eye-Brain disease with multicystic leucodystrophy results in ER-retention of the mutant protein Signorino, Giulia; Covaceuszach, Sonia; Bozzi, Manuela; Hubner, Wolfgang; Mönkemöller, Viola; Konarev, Petr V; Cassetta, Alberto; Brancaccio, Andrea; Sciandra, Francesca
1-gen-2017 alpha-Dystroglycan hypoglycosylation affects cell migration by influencing beta-dystroglycan membrane clustering and filopodia length: A multiscale confocal microscopy analysis Palmieri, V.; Bozzi, M.; Signorino, G.; Papi, M.; De Spirito, M.; Brancaccio, A.; Maulucci, G.; Sciandra, F.
1-gen-2017 Evaluation of the effect of a floxed Neo cassette within the dystroglycan (Dag1) gene Sciandra, Francesca; Scicchitano, Bianca Maria; Signorino, Giulia; Bigotti, Maria Giulia; Tavazzi, Barbara; Lombardi, Francesca; Bozzi, Manuela; Sica, Gigliola; Giardina, Bruno; Blaess, Sandra; Brancaccio, Andrea
1-gen-2017 Structural flexibility of human alpha-dystroglycan Covaceuszach, Sonia; Bozzi, Manuela; Bigotti, Maria Giulia; Sciandra, Francesca; Konarev, Petr Valeryevich; Brancaccio, Andrea; Cassetta, Alberto
1-gen-2017 The effect of the pathological V72I, D109N and T190M missense mutations on the molecular structure of alpha-dystroglycan Covaceuszach, Sonia; Bozzi, Manuela; Bigotti, Maria Giulia; Sciandra, Francesca; Konarev, Petr V.; Brancaccio, Andrea; Cassetta, Alberto
1-gen-2015 Alpha-Dystroglycan is a Potential Target of Matrix Metalloproteinase MMP-2 Sbardella, D; Sciandra, Francesca; Gioia, M; Marini, S; Gori, A; Giardina, B; Tarantino, U; Coletta, M; Brancaccio, Andrea; Bozzi, Manuela
1-gen-2015 Genetic Engineering of Dystroglycan in Animal Models of Muscular Dystrophy Sciandra, Francesca; Bigotti, Maria Giulia; Giardina, Bruno; Bozzi, Manuela; Brancaccio, Andrea
1-gen-2015 Role of gelatinases in pathological and physiological processes involving the dystrophin-glycoprotein complex Bozzi, Manuela; Sciandra, Francesca; Brancaccio, Andrea
1-gen-2015 The Structure of the T190M Mutant of Murine α-Dystroglycan at High Resolution: Insight into the Molecular Basis of a Primary Dystroglycanopathy Bozzi, Manuela; Cassetta, A; Covaceuszach, S; Bigotti, Mg; Bannister, S; Hubner, W; Sciandra, Francesca; Lamba, D; Brancaccio, Andrea
1-gen-2014 Insights from molecular dynamics simulations: structural basis for the V567D mutation-induced instability of zebrafish alpha-dystroglycan and comparison with the murine model. Pirolli, Davide; Sciandra, Francesca; Bozzi, Manuela; Giardina, Bruno; Brancaccio, Andrea; De Rosa, Maria Cristina
1-gen-2013 The multiple affinities of α-dystroglycan Sciandra, Francesca; Bozzi, Manuela; Bigotti, M. G.; Brancaccio, Andrea
1-gen-2012 Dystroglycan is associated to the disulfide isomerase ERp57 Sciandra, Francesca; Angelucci, Emanuela; Altieri, Fabio; Ricci, Daniela; Huebner, Wolfgang; Petrucci, Tamara; Giardina, Bruno; Brancaccio, Andrea; Bozzi, Manuela
1-gen-2012 Enzymatic processing by MMP-2 and MMP-9 of wild-type and mutated mouse ss-dystroglycan Sbardella, D; Inzitari, Rosanna; Iavarone, Federica; Gioia, M; Marini, S; Sciandra, F; Castagnola, Massimo; Van Den Steen, Pe; Opdenakker, G; Giardina, Bruno; Brancaccio, Andrea; Coletta, M; Bozzi, Manuela
1-gen-2012 Insertion of a myc-tag within alpha-dystroglycan domains improves its biochemical and microscopic detection Morlacchi, Simona; Sciandra, Francesca; Bigotti, Maria Giulia; Bozzi, Manuela; Hubner, Wolfgang; Galtieri, Antonio; Giardina, Bruno; Brancaccio, Andrea
1-gen-2011 A second Ig-like domain identified in dystroglycan by molecular modelling and dynamics De Rosa, Maria Cristina; Pirolli, Davide; Bozzi, Manuela; Sciandra, Francesca; Giardina, Bruno; Brancaccio, Andrea