Brancaccio, Andrea
Dettaglio
Brancaccio, Andrea
Pubblicazioni
Risultati 1 - 20 di 27 (tempo di esecuzione: 0.001 secondi).
Data di pubblicazione | Titolo | Autore(i) | File | |
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1 | 2020 | Identification and modelling of a GT-A fold in the α-dystroglycan glycosylating enzyme LARGE1 | Righino, Benedetta; Bozzi, Manuela; Pirolli, Davide; Sciandra, Francesca; Bigotti, Maria Giulia; Brancaccio, Andrea; De Rosa, Maria Cristina | - |
2 | 2018 | The enzymatic processing of α-dystroglycan by MMP-2 is controlled by two anchoring sites distinct from the active site. | Gioia, Magda; Francesco Fasciglione, Giovanni; Sbardella, Diego; Sciandra, Francesca; Casella, Marialuisa; Camerini, Serena; Crescenzi, Marco; Gori, Alessandro; Tarantino, Umberto; Cozza, Paola; Brancaccio, Andrea; Coletta, Massimo; Bozzi, Manuela | Open Access |
3 | 2017 | A dystroglycan mutation (p.Cys667Phe) associated to Muscle-Eye-Brain disease with multicystic leucodystrophy results in ER-retention of the mutant protein | Signorino, Giulia; Covaceuszach, Sonia; Bozzi, Manuela; Hubner, Wolfgang; Mönkemöller, Viola; Konarev, Petr V; Cassetta, Alberto; Brancaccio, Andrea; Sciandra, Francesca | - |
4 | 2017 | alpha-Dystroglycan hypoglycosylation affects cell migration by influencing beta-dystroglycan membrane clustering and filopodia length: A multiscale confocal microscopy analysis | Palmieri, V.; Bozzi, M.; Signorino, G.; Papi, M.; De Spirito, M.; Brancaccio, A.; Maulucci, G.; Sciandra, F. | - |
5 | 2017 | Evaluation of the effect of a floxed Neo cassette within the dystroglycan (Dag1) gene | Sciandra, Francesca; Scicchitano, Bianca Maria; Signorino, Giulia; Bigotti, Maria Giulia; Tavazzi, Barbara; Lombardi, Francesca; Bozzi, Manuela; Sica, Gigliola; Giardina, Bruno; Blaess, Sandra; Brancaccio, Andrea | Open Access |
6 | 2017 | Structural flexibility of human alpha-dystroglycan | Covaceuszach, Sonia; Bozzi, Manuela; Bigotti, Maria Giulia; Sciandra, Francesca; Konarev, Petr Valeryevich; Brancaccio, Andrea; Cassetta, Alberto | Open Access |
7 | 2017 | The effect of the pathological V72I, D109N and T190M missense mutations on the molecular structure of alpha-dystroglycan | Covaceuszach, Sonia; Bozzi, Manuela; Bigotti, Maria Giulia; Sciandra, Francesca; Konarev, Petr V.; Brancaccio, Andrea; Cassetta, Alberto | Open Access |
8 | 2015 | Alpha-Dystroglycan is a Potential Target of Matrix Metalloproteinase MMP-2 | Sbardella, D; Sciandra, Francesca; Gioia, M; Marini, S; Gori, A; Giardina, B; Tarantino, U; Coletta, M; Brancaccio, Andrea; Bozzi, Manuela | - |
9 | 2015 | Genetic Engineering of Dystroglycan in Animal Models of Muscular Dystrophy | Sciandra, Francesca; Bigotti, Maria Giulia; Giardina, Bruno; Bozzi, Manuela; Brancaccio, Andrea | Open Access |
10 | 2015 | Role of gelatinases in pathological and physiological processes involving the dystrophin-glycoprotein complex | Bozzi, Manuela; Sciandra, Francesca; Brancaccio, Andrea | Open Access |
11 | 2015 | The Structure of the T190M Mutant of Murine α-Dystroglycan at High Resolution: Insight into the Molecular Basis of a Primary Dystroglycanopathy | Bozzi, Manuela; Cassetta, A; Covaceuszach, S; Bigotti, Mg; Bannister, S; Hubner, W; Sciandra, Francesca; Lamba, D; Brancaccio, Andrea | Open Access |
12 | 2014 | Insights from molecular dynamics simulations: structural basis for the V567D mutation-induced instability of zebrafish alpha-dystroglycan and comparison with the murine model. | Pirolli, Davide; Sciandra, Francesca; Bozzi, Manuela; Giardina, Bruno; Brancaccio, Andrea; De Rosa, Maria Cristina | Open Access |
13 | 2013 | The multiple affinities of α-dystroglycan | Sciandra, F.; Bozzi, M.; Bigotti, M. G.; Brancaccio, A. | - |
14 | 2012 | Dystroglycan is associated to the disulfide isomerase ERp57 | Sciandra, Francesca; Angelucci, Emanuela; Altieri, Fabio; Ricci, Daniela; Huebner, Wolfgang; Petrucci, Tamara; Giardina, Bruno; Brancaccio, Andrea; Bozzi, Manuela | - |
15 | 2012 | Enzymatic processing by MMP-2 and MMP-9 of wild-type and mutated mouse ss-dystroglycan | Sbardella, D; Inzitari, Rosanna; Iavarone, Federica; Gioia, M; Marini, S; Sciandra, F; Castagnola, Massimo; Van Den Steen, Pe; Opdenakker, G; Giardina, Bruno; Brancaccio, Andrea; Coletta, M; Bozzi, Manuela | - |
16 | 2012 | Insertion of a myc-tag within alpha-dystroglycan domains improves its biochemical and microscopic detection | Morlacchi, Simona; Sciandra, Francesca; Bigotti, Maria Giulia; Bozzi, Manuela; Hubner, Wolfgang; Galtieri, Antonio; Giardina, Bruno; Brancaccio, Andrea | - |
17 | 2011 | A second Ig-like domain identified in dystroglycan by molecular modelling and dynamics | De Rosa, Maria Cristina; Pirolli, Davide; Bozzi, Manuela; Sciandra, Francesca; Giardina, Bruno; Brancaccio, Andrea | - |
18 | 2011 | An immunological analysis of dystroglycan subunits: lessons learned from a small cohort of non-congenital dystrophic patients. | Pavoni, Ernesto; Sciandra, Francesca; Tasca, Giorgio; Tittarelli, Roberta; Bozzi, Manuela; Ricci, Enzo; Brancaccio, Andrea | Open Access |
19 | 2011 | Insertion of 16 amino acids in the BAR domain of the oligophrenin 1 protein causes mental retardation and cerebellar hypoplasia in an Italian family | Pirozzi, Filomena; Di Raimo, Francesca Romana; Zanni, G; Bertini, E; Billuart, P; Tartaglione, Tommaso; Tabolacci, Elisabetta; Brancaccio, Andrea; Neri, Giovanni; Chiurazzi, Pietro | - |
20 | 2009 | Enzymatic processing of beta-destroglycan recombinant ectodomain by MMP-9: identification of the main cleavage site. | Bozzi, Manuela; Inzitari, Rosanna; Sbardella, Diego; Monaco, Susanna; Pavoni, Ernesto; Gioia, Magda; Marini, Stefano; Morlacchi, Simona; Sciandra, Francesca; Castagnola, Massimo; Giardina, Bruno; Brancaccio, Andrea; Coletta, Massimiliano | - |