Sciandra, Francesca

Sciandra, Francesca  

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Data di pubblicazione Titolo Autore(i) File
1-gen-2023 Verbascoside Elicits Its Beneficial Effects by Enhancing Mitochondrial Spare Respiratory Capacity and the Nrf2/HO-1 Mediated Antioxidant System in a Murine Skeletal Muscle Cell Line Sciandra, Francesca; Bottoni, Paola; De Leo, M.; Braca, A.; Brancaccio, Andrea; Bozzi, Manuela
1-gen-2022 3D-printed graphene polylactic acid devices resistant to SARS-CoV-2: Sunlight-mediated sterilization of additive manufactured objects De Maio, Flavio; Rosa, Enrico; Perini, Giordano; Augello, A; Niccolini, Benedetta; Ciaiola, F; Santarelli, Giulia; Sciandra, Francesca; Bozzi, Manuela; Sanguinetti, Maurizio; Sali, Michela; De Spirito, Marco; Delogu, Giovanni; Palmieri, Valentina; Papi, Massimiliano
1-gen-2021 Discovery of 4-benzyloxy and 4-(2-phenylethoxy) chalcone fibrate hybrids as novel PPARα agonists with anti-hyperlipidemic and antioxidant activities: Design, synthesis and in vitro/in vivo biological evaluation Hassan, R. M.; Aboutabl, M. E.; Bozzi, Manuela; El-Behairy, M. F.; El Kerdawy, A. M.; Sampaolese, B.; Desiderio, Claudia; Vincenzoni, F.; Sciandra, Francesca; Ghannam, I. A. Y.
1-gen-2020 3D graphene scaffolds for skeletal muscle regeneration: future perspectives Palmieri, Valentina; Sciandra, Francesca; Bozzi, Manuela; De Spirito, Marco; Papi, Massimiliano
1-gen-2020 Identification and modelling of a GT-A fold in the α-dystroglycan glycosylating enzyme LARGE1 Righino, Benedetta; Bozzi, Manuela; Pirolli, Davide; Sciandra, Francesca; Bigotti, Maria Giulia; Brancaccio, Andrea; De Rosa, Maria Cristina
1-gen-2020 Molecular mechanisms underlying muscle wasting in huntington’s disease Bozzi, Manuela; Sciandra, Francesca
1-gen-2020 Punicalagin protects human retinal pigment epithelium cells from ultraviolet radiation-induced oxidative damage by activating nrf2/ho-1 signaling pathway and reducing apoptosis Clementi, Maria Elisabetta; Sampaolese, B.; Sciandra, Francesca; Tringali, Giuseppe
1-gen-2018 The enzymatic processing of α-dystroglycan by MMP-2 is controlled by two anchoring sites distinct from the active site. Gioia, Magda; Francesco Fasciglione, Giovanni; Sbardella, Diego; Sciandra, Francesca; Casella, Marialuisa; Camerini, Serena; Crescenzi, Marco; Gori, Alessandro; Tarantino, Umberto; Cozza, Paola; Brancaccio, Andrea; Coletta, Massimo; Bozzi, Manuela
1-gen-2017 A dystroglycan mutation (p.Cys667Phe) associated to Muscle-Eye-Brain disease with multicystic leucodystrophy results in ER-retention of the mutant protein Signorino, Giulia; Covaceuszach, Sonia; Bozzi, Manuela; Hubner, Wolfgang; Mönkemöller, Viola; Konarev, Petr V; Cassetta, Alberto; Brancaccio, Andrea; Sciandra, Francesca
1-gen-2017 alpha-Dystroglycan hypoglycosylation affects cell migration by influencing beta-dystroglycan membrane clustering and filopodia length: A multiscale confocal microscopy analysis Palmieri, V.; Bozzi, M.; Signorino, G.; Papi, M.; De Spirito, M.; Brancaccio, A.; Maulucci, G.; Sciandra, F.
1-gen-2017 Evaluation of the effect of a floxed Neo cassette within the dystroglycan (Dag1) gene Sciandra, Francesca; Scicchitano, Bianca Maria; Signorino, Giulia; Bigotti, Maria Giulia; Tavazzi, Barbara; Lombardi, Francesca; Bozzi, Manuela; Sica, Gigliola; Giardina, Bruno; Blaess, Sandra; Brancaccio, Andrea
1-gen-2017 Structural flexibility of human alpha-dystroglycan Covaceuszach, Sonia; Bozzi, Manuela; Bigotti, Maria Giulia; Sciandra, Francesca; Konarev, Petr Valeryevich; Brancaccio, Andrea; Cassetta, Alberto
1-gen-2017 The effect of the pathological V72I, D109N and T190M missense mutations on the molecular structure of alpha-dystroglycan Covaceuszach, Sonia; Bozzi, Manuela; Bigotti, Maria Giulia; Sciandra, Francesca; Konarev, Petr V.; Brancaccio, Andrea; Cassetta, Alberto
1-gen-2015 Alpha-Dystroglycan is a Potential Target of Matrix Metalloproteinase MMP-2 Sbardella, D; Sciandra, Francesca; Gioia, M; Marini, S; Gori, A; Giardina, B; Tarantino, U; Coletta, M; Brancaccio, Andrea; Bozzi, Manuela
1-gen-2015 Genetic Engineering of Dystroglycan in Animal Models of Muscular Dystrophy Sciandra, Francesca; Bigotti, Maria Giulia; Giardina, Bruno; Bozzi, Manuela; Brancaccio, Andrea
1-gen-2015 Role of gelatinases in pathological and physiological processes involving the dystrophin-glycoprotein complex Bozzi, Manuela; Sciandra, Francesca; Brancaccio, Andrea
1-gen-2015 The Structure of the T190M Mutant of Murine α-Dystroglycan at High Resolution: Insight into the Molecular Basis of a Primary Dystroglycanopathy Bozzi, Manuela; Cassetta, A; Covaceuszach, S; Bigotti, Mg; Bannister, S; Hubner, W; Sciandra, Francesca; Lamba, D; Brancaccio, Andrea
1-gen-2014 Insights from molecular dynamics simulations: structural basis for the V567D mutation-induced instability of zebrafish alpha-dystroglycan and comparison with the murine model. Pirolli, Davide; Sciandra, Francesca; Bozzi, Manuela; Giardina, Bruno; Brancaccio, Andrea; De Rosa, Maria Cristina
1-gen-2013 The multiple affinities of α-dystroglycan Sciandra, Francesca; Bozzi, Manuela; Bigotti, M. G.; Brancaccio, Andrea
1-gen-2011 An immunological analysis of dystroglycan subunits: Lessons learned from a small cohort of non-congenital dystrophic patients Pavoni, Ernesto; Sciandra, Francesca; Tasca, Giorgio; Tittarelli, R.; Bozzi, Manuela; Giardina, Bruno; Ricci, Enzo; Brancaccio, Andrea