Sciandra, Francesca
Dettaglio
Sciandra, Francesca
Pubblicazioni
Risultati 1 - 16 di 16 (tempo di esecuzione: 0.001 secondi).
Data di pubblicazione | Titolo | Autore(i) | File | |
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1 | 2020 | Identification and modelling of a GT-A fold in the α-dystroglycan glycosylating enzyme LARGE1 | Righino, Benedetta; Bozzi, Manuela; Pirolli, Davide; Sciandra, Francesca; Bigotti, Maria Giulia; Brancaccio, Andrea; De Rosa, Maria Cristina | - |
2 | 2020 | Molecular mechanisms underlying muscle wasting in huntington’s disease | Bozzi, M.; Sciandra, F. | - |
3 | 2020 | Punicalagin protects human retinal pigment epithelium cells from ultraviolet radiation-induced oxidative damage by activating nrf2/ho-1 signaling pathway and reducing apoptosis | Clementi, M. E.; Sampaolese, B.; Sciandra, F.; Tringali, G. | - |
4 | 2020 | 3D graphene scaffolds for skeletal muscle regeneration: future perspectives | Palmieri, Valentina; Sciandra, Francesca; Bozzi, Manuela; De Spirito, Marco; Papi, Massimiliano | Open Access |
5 | 2018 | The enzymatic processing of α-dystroglycan by MMP-2 is controlled by two anchoring sites distinct from the active site. | Gioia, Magda; Francesco Fasciglione, Giovanni; Sbardella, Diego; Sciandra, Francesca; Casella, Marialuisa; Camerini, Serena; Crescenzi, Marco; Gori, Alessandro; Tarantino, Umberto; Cozza, Paola; Brancaccio, Andrea; Coletta, Massimo; Bozzi, Manuela | Open Access |
6 | 2017 | A dystroglycan mutation (p.Cys667Phe) associated to Muscle-Eye-Brain disease with multicystic leucodystrophy results in ER-retention of the mutant protein | Signorino, Giulia; Covaceuszach, Sonia; Bozzi, Manuela; Hubner, Wolfgang; Mönkemöller, Viola; Konarev, Petr V; Cassetta, Alberto; Brancaccio, Andrea; Sciandra, Francesca | - |
7 | 2017 | alpha-Dystroglycan hypoglycosylation affects cell migration by influencing beta-dystroglycan membrane clustering and filopodia length: A multiscale confocal microscopy analysis | Palmieri, V.; Bozzi, M.; Signorino, G.; Papi, M.; De Spirito, M.; Brancaccio, A.; Maulucci, G.; Sciandra, F. | - |
8 | 2017 | Evaluation of the effect of a floxed Neo cassette within the dystroglycan (Dag1) gene | Sciandra, Francesca; Scicchitano, Bianca Maria; Signorino, Giulia; Bigotti, Maria Giulia; Tavazzi, Barbara; Lombardi, Francesca; Bozzi, Manuela; Sica, Gigliola; Giardina, Bruno; Blaess, Sandra; Brancaccio, Andrea | Open Access |
9 | 2017 | Structural flexibility of human alpha-dystroglycan | Covaceuszach, Sonia; Bozzi, Manuela; Bigotti, Maria Giulia; Sciandra, Francesca; Konarev, Petr Valeryevich; Brancaccio, Andrea; Cassetta, Alberto | Open Access |
10 | 2017 | The effect of the pathological V72I, D109N and T190M missense mutations on the molecular structure of alpha-dystroglycan | Covaceuszach, Sonia; Bozzi, Manuela; Bigotti, Maria Giulia; Sciandra, Francesca; Konarev, Petr V.; Brancaccio, Andrea; Cassetta, Alberto | Open Access |
11 | 2015 | Alpha-Dystroglycan is a Potential Target of Matrix Metalloproteinase MMP-2 | Sbardella, D; Sciandra, Francesca; Gioia, M; Marini, S; Gori, A; Giardina, B; Tarantino, U; Coletta, M; Brancaccio, Andrea; Bozzi, Manuela | - |
12 | 2015 | Genetic Engineering of Dystroglycan in Animal Models of Muscular Dystrophy | Sciandra, Francesca; Bigotti, Maria Giulia; Giardina, Bruno; Bozzi, Manuela; Brancaccio, Andrea | Open Access |
13 | 2015 | Role of gelatinases in pathological and physiological processes involving the dystrophin-glycoprotein complex | Bozzi, Manuela; Sciandra, Francesca; Brancaccio, Andrea | Open Access |
14 | 2015 | The Structure of the T190M Mutant of Murine α-Dystroglycan at High Resolution: Insight into the Molecular Basis of a Primary Dystroglycanopathy | Bozzi, Manuela; Cassetta, A; Covaceuszach, S; Bigotti, Mg; Bannister, S; Hubner, W; Sciandra, Francesca; Lamba, D; Brancaccio, Andrea | Open Access |
15 | 2014 | Insights from molecular dynamics simulations: structural basis for the V567D mutation-induced instability of zebrafish alpha-dystroglycan and comparison with the murine model. | Pirolli, Davide; Sciandra, Francesca; Bozzi, Manuela; Giardina, Bruno; Brancaccio, Andrea; De Rosa, Maria Cristina | Open Access |
16 | 2013 | The multiple affinities of α-dystroglycan | Sciandra, F.; Bozzi, M.; Bigotti, M. G.; Brancaccio, A. | - |