Sciandra, Francesca
Sciandra, Francesca
Verbascoside Elicits Its Beneficial Effects by Enhancing Mitochondrial Spare Respiratory Capacity and the Nrf2/HO-1 Mediated Antioxidant System in a Murine Skeletal Muscle Cell Line
2023 Sciandra, Francesca; Bottoni, Paola; De Leo, M.; Braca, A.; Brancaccio, Andrea; Bozzi, Manuela
3D-printed graphene polylactic acid devices resistant to SARS-CoV-2: Sunlight-mediated sterilization of additive manufactured objects
2022 De Maio, Flavio; Rosa, Enrico; Perini, Giordano; Augello, A; Niccolini, Benedetta; Ciaiola, F; Santarelli, Giulia; Sciandra, Francesca; Bozzi, Manuela; Sanguinetti, Maurizio; Sali, Michela; De Spirito, Marco; Delogu, Giovanni; Palmieri, Valentina; Papi, Massimiliano
Discovery of 4-benzyloxy and 4-(2-phenylethoxy) chalcone fibrate hybrids as novel PPARα agonists with anti-hyperlipidemic and antioxidant activities: Design, synthesis and in vitro/in vivo biological evaluation
2021 Hassan, R. M.; Aboutabl, M. E.; Bozzi, Manuela; El-Behairy, M. F.; El Kerdawy, A. M.; Sampaolese, B.; Desiderio, Claudia; Vincenzoni, F.; Sciandra, Francesca; Ghannam, I. A. Y.
3D graphene scaffolds for skeletal muscle regeneration: future perspectives
2020 Palmieri, Valentina; Sciandra, Francesca; Bozzi, Manuela; De Spirito, Marco; Papi, Massimiliano
Identification and modelling of a GT-A fold in the α-dystroglycan glycosylating enzyme LARGE1
2020 Righino, Benedetta; Bozzi, Manuela; Pirolli, Davide; Sciandra, Francesca; Bigotti, Maria Giulia; Brancaccio, Andrea; De Rosa, Maria Cristina
Molecular mechanisms underlying muscle wasting in huntington’s disease
2020 Bozzi, Manuela; Sciandra, Francesca
Punicalagin protects human retinal pigment epithelium cells from ultraviolet radiation-induced oxidative damage by activating nrf2/ho-1 signaling pathway and reducing apoptosis
2020 Clementi, Maria Elisabetta; Sampaolese, B.; Sciandra, Francesca; Tringali, Giuseppe
The enzymatic processing of α-dystroglycan by MMP-2 is controlled by two anchoring sites distinct from the active site.
2018 Gioia, Magda; Francesco Fasciglione, Giovanni; Sbardella, Diego; Sciandra, Francesca; Casella, Marialuisa; Camerini, Serena; Crescenzi, Marco; Gori, Alessandro; Tarantino, Umberto; Cozza, Paola; Brancaccio, Andrea; Coletta, Massimo; Bozzi, Manuela
A dystroglycan mutation (p.Cys667Phe) associated to Muscle-Eye-Brain disease with multicystic leucodystrophy results in ER-retention of the mutant protein
2017 Signorino, Giulia; Covaceuszach, Sonia; Bozzi, Manuela; Hubner, Wolfgang; Mönkemöller, Viola; Konarev, Petr V; Cassetta, Alberto; Brancaccio, Andrea; Sciandra, Francesca
alpha-Dystroglycan hypoglycosylation affects cell migration by influencing beta-dystroglycan membrane clustering and filopodia length: A multiscale confocal microscopy analysis
2017 Palmieri, V.; Bozzi, M.; Signorino, G.; Papi, M.; De Spirito, M.; Brancaccio, A.; Maulucci, G.; Sciandra, F.
Evaluation of the effect of a floxed Neo cassette within the dystroglycan (Dag1) gene
2017 Sciandra, Francesca; Scicchitano, Bianca Maria; Signorino, Giulia; Bigotti, Maria Giulia; Tavazzi, Barbara; Lombardi, Francesca; Bozzi, Manuela; Sica, Gigliola; Giardina, Bruno; Blaess, Sandra; Brancaccio, Andrea
Structural flexibility of human alpha-dystroglycan
2017 Covaceuszach, Sonia; Bozzi, Manuela; Bigotti, Maria Giulia; Sciandra, Francesca; Konarev, Petr Valeryevich; Brancaccio, Andrea; Cassetta, Alberto
The effect of the pathological V72I, D109N and T190M missense mutations on the molecular structure of alpha-dystroglycan
2017 Covaceuszach, Sonia; Bozzi, Manuela; Bigotti, Maria Giulia; Sciandra, Francesca; Konarev, Petr V.; Brancaccio, Andrea; Cassetta, Alberto
Alpha-Dystroglycan is a Potential Target of Matrix Metalloproteinase MMP-2
2015 Sbardella, D; Sciandra, Francesca; Gioia, M; Marini, S; Gori, A; Giardina, B; Tarantino, U; Coletta, M; Brancaccio, Andrea; Bozzi, Manuela
Genetic Engineering of Dystroglycan in Animal Models of Muscular Dystrophy
2015 Sciandra, Francesca; Bigotti, Maria Giulia; Giardina, Bruno; Bozzi, Manuela; Brancaccio, Andrea
Role of gelatinases in pathological and physiological processes involving the dystrophin-glycoprotein complex
2015 Bozzi, Manuela; Sciandra, Francesca; Brancaccio, Andrea
The Structure of the T190M Mutant of Murine α-Dystroglycan at High Resolution: Insight into the Molecular Basis of a Primary Dystroglycanopathy
2015 Bozzi, Manuela; Cassetta, A; Covaceuszach, S; Bigotti, Mg; Bannister, S; Hubner, W; Sciandra, Francesca; Lamba, D; Brancaccio, Andrea
Insights from molecular dynamics simulations: structural basis for the V567D mutation-induced instability of zebrafish alpha-dystroglycan and comparison with the murine model.
2014 Pirolli, Davide; Sciandra, Francesca; Bozzi, Manuela; Giardina, Bruno; Brancaccio, Andrea; De Rosa, Maria Cristina
The multiple affinities of α-dystroglycan
2013 Sciandra, Francesca; Bozzi, Manuela; Bigotti, M. G.; Brancaccio, Andrea
An immunological analysis of dystroglycan subunits: Lessons learned from a small cohort of non-congenital dystrophic patients
2011 Pavoni, Ernesto; Sciandra, Francesca; Tasca, Giorgio; Tittarelli, R.; Bozzi, Manuela; Giardina, Bruno; Ricci, Enzo; Brancaccio, Andrea
Data di pubblicazione | Titolo | Autore(i) | File |
---|---|---|---|
1-gen-2023 | Verbascoside Elicits Its Beneficial Effects by Enhancing Mitochondrial Spare Respiratory Capacity and the Nrf2/HO-1 Mediated Antioxidant System in a Murine Skeletal Muscle Cell Line | Sciandra, Francesca; Bottoni, Paola; De Leo, M.; Braca, A.; Brancaccio, Andrea; Bozzi, Manuela | |
1-gen-2022 | 3D-printed graphene polylactic acid devices resistant to SARS-CoV-2: Sunlight-mediated sterilization of additive manufactured objects | De Maio, Flavio; Rosa, Enrico; Perini, Giordano; Augello, A; Niccolini, Benedetta; Ciaiola, F; Santarelli, Giulia; Sciandra, Francesca; Bozzi, Manuela; Sanguinetti, Maurizio; Sali, Michela; De Spirito, Marco; Delogu, Giovanni; Palmieri, Valentina; Papi, Massimiliano | |
1-gen-2021 | Discovery of 4-benzyloxy and 4-(2-phenylethoxy) chalcone fibrate hybrids as novel PPARα agonists with anti-hyperlipidemic and antioxidant activities: Design, synthesis and in vitro/in vivo biological evaluation | Hassan, R. M.; Aboutabl, M. E.; Bozzi, Manuela; El-Behairy, M. F.; El Kerdawy, A. M.; Sampaolese, B.; Desiderio, Claudia; Vincenzoni, F.; Sciandra, Francesca; Ghannam, I. A. Y. | |
1-gen-2020 | 3D graphene scaffolds for skeletal muscle regeneration: future perspectives | Palmieri, Valentina; Sciandra, Francesca; Bozzi, Manuela; De Spirito, Marco; Papi, Massimiliano | |
1-gen-2020 | Identification and modelling of a GT-A fold in the α-dystroglycan glycosylating enzyme LARGE1 | Righino, Benedetta; Bozzi, Manuela; Pirolli, Davide; Sciandra, Francesca; Bigotti, Maria Giulia; Brancaccio, Andrea; De Rosa, Maria Cristina | |
1-gen-2020 | Molecular mechanisms underlying muscle wasting in huntington’s disease | Bozzi, Manuela; Sciandra, Francesca | |
1-gen-2020 | Punicalagin protects human retinal pigment epithelium cells from ultraviolet radiation-induced oxidative damage by activating nrf2/ho-1 signaling pathway and reducing apoptosis | Clementi, Maria Elisabetta; Sampaolese, B.; Sciandra, Francesca; Tringali, Giuseppe | |
1-gen-2018 | The enzymatic processing of α-dystroglycan by MMP-2 is controlled by two anchoring sites distinct from the active site. | Gioia, Magda; Francesco Fasciglione, Giovanni; Sbardella, Diego; Sciandra, Francesca; Casella, Marialuisa; Camerini, Serena; Crescenzi, Marco; Gori, Alessandro; Tarantino, Umberto; Cozza, Paola; Brancaccio, Andrea; Coletta, Massimo; Bozzi, Manuela | |
1-gen-2017 | A dystroglycan mutation (p.Cys667Phe) associated to Muscle-Eye-Brain disease with multicystic leucodystrophy results in ER-retention of the mutant protein | Signorino, Giulia; Covaceuszach, Sonia; Bozzi, Manuela; Hubner, Wolfgang; Mönkemöller, Viola; Konarev, Petr V; Cassetta, Alberto; Brancaccio, Andrea; Sciandra, Francesca | |
1-gen-2017 | alpha-Dystroglycan hypoglycosylation affects cell migration by influencing beta-dystroglycan membrane clustering and filopodia length: A multiscale confocal microscopy analysis | Palmieri, V.; Bozzi, M.; Signorino, G.; Papi, M.; De Spirito, M.; Brancaccio, A.; Maulucci, G.; Sciandra, F. | |
1-gen-2017 | Evaluation of the effect of a floxed Neo cassette within the dystroglycan (Dag1) gene | Sciandra, Francesca; Scicchitano, Bianca Maria; Signorino, Giulia; Bigotti, Maria Giulia; Tavazzi, Barbara; Lombardi, Francesca; Bozzi, Manuela; Sica, Gigliola; Giardina, Bruno; Blaess, Sandra; Brancaccio, Andrea | |
1-gen-2017 | Structural flexibility of human alpha-dystroglycan | Covaceuszach, Sonia; Bozzi, Manuela; Bigotti, Maria Giulia; Sciandra, Francesca; Konarev, Petr Valeryevich; Brancaccio, Andrea; Cassetta, Alberto | |
1-gen-2017 | The effect of the pathological V72I, D109N and T190M missense mutations on the molecular structure of alpha-dystroglycan | Covaceuszach, Sonia; Bozzi, Manuela; Bigotti, Maria Giulia; Sciandra, Francesca; Konarev, Petr V.; Brancaccio, Andrea; Cassetta, Alberto | |
1-gen-2015 | Alpha-Dystroglycan is a Potential Target of Matrix Metalloproteinase MMP-2 | Sbardella, D; Sciandra, Francesca; Gioia, M; Marini, S; Gori, A; Giardina, B; Tarantino, U; Coletta, M; Brancaccio, Andrea; Bozzi, Manuela | |
1-gen-2015 | Genetic Engineering of Dystroglycan in Animal Models of Muscular Dystrophy | Sciandra, Francesca; Bigotti, Maria Giulia; Giardina, Bruno; Bozzi, Manuela; Brancaccio, Andrea | |
1-gen-2015 | Role of gelatinases in pathological and physiological processes involving the dystrophin-glycoprotein complex | Bozzi, Manuela; Sciandra, Francesca; Brancaccio, Andrea | |
1-gen-2015 | The Structure of the T190M Mutant of Murine α-Dystroglycan at High Resolution: Insight into the Molecular Basis of a Primary Dystroglycanopathy | Bozzi, Manuela; Cassetta, A; Covaceuszach, S; Bigotti, Mg; Bannister, S; Hubner, W; Sciandra, Francesca; Lamba, D; Brancaccio, Andrea | |
1-gen-2014 | Insights from molecular dynamics simulations: structural basis for the V567D mutation-induced instability of zebrafish alpha-dystroglycan and comparison with the murine model. | Pirolli, Davide; Sciandra, Francesca; Bozzi, Manuela; Giardina, Bruno; Brancaccio, Andrea; De Rosa, Maria Cristina | |
1-gen-2013 | The multiple affinities of α-dystroglycan | Sciandra, Francesca; Bozzi, Manuela; Bigotti, M. G.; Brancaccio, Andrea | |
1-gen-2011 | An immunological analysis of dystroglycan subunits: Lessons learned from a small cohort of non-congenital dystrophic patients | Pavoni, Ernesto; Sciandra, Francesca; Tasca, Giorgio; Tittarelli, R.; Bozzi, Manuela; Giardina, Bruno; Ricci, Enzo; Brancaccio, Andrea |